The variations in the structure and position of the kidney along with variations of renal vessels are reported by anatomists, surgeons and radiologists. Routine human cadaveric dissection showed a bilateral ectopic kidney with accessory renal artery was observed. Malrotation of both kidneys and altered anatomical structures in the hilum were observed. The both kidneys are located above the bifurcation of common lilac arteries. The Accessory renal arteries were arising from the abdominal aorta and supply both the kidneys. The renal veins draining into inferior venacava. Ectopic kidney with rotational variation of accessory renal arteries is comparatively very rare. This may be asymptomatic or present with vague symptoms and sometimes remain unknown during the lifetime. These variations have an embryological basis and are clinically significant. Knowing such variations are important for general surgeons, gynecologists for performing various surgical procedures like laparoscopic surgeries and useful for the nephrologists when dealing with radical nephrectomy and renal transplantations