Ocular colobomas are malformations of eye and are associated with early cataractous changes. Cataract surgery in eyes with coloboma require extra care and planning at each stage as these eyes are at greater risk for complications during cataract surgery. Presenting here, the outcome of cataract surgery in a 45 years female who presented with micro cornea, iris coloboma and advanced cataractous changes with nystagmus. The preoperative planning and management, the complications dealt during phacoemulsification and the outcome are discussed.