Introduction: Behçet disease is a systemic inflammatory disease characterized by intraocular inflammation, oral and genital ulcers, skin lesions and many other visceral disorders. It is particularly prevalent in the countries of the Mediterranean basin and in the Middle East. The objective of our work is to describe clinical, therapeutic and prognostic characteristics of ocular Behçet disease. Methods: We present a retrospective study of 14 patients with ocular Behçet disease, diagnosed according to the International Study Group of Behçet disease criteria. All patients underwent a complete ophthalmologic examination, Fluorescein Angiography and Optical Coherence Tomography OCT. Results: The average age is 32.5 years, ranging from 17 to 64 years. A male predominance was noted. Visual acuity was > 1/10 in 8 patients, between 1/10 and 5/10 in 4 patients and > 5/10 in 2 patients. Ophthalmological examination revealed an anterior non-granulomatous uveitis in 8 patients, with hypopyon in 2 patients and with acute hypertonia in 2 others, an intermediate uveitis with hyalitis in 2 patients, a retinal vasculitis with periphlebitis in 3 patients, a branch retinal venous occlusion in 1 patient; a macular edema in 2 patients and a papillary edema in 3 patients. Fluorescein Angiography objectified vasculitis with white sheathing end tortuous vessels in 3 cases, peripheral retinal ischemia in 1 patient and papillitis with late diffusion in 3 cases. Macular OCT showed cystoid macular edema in 2 cases. Therapeutic management consisted of topical corticotherapy with mydriatics in isolated anterior inflammation. A bolus of Solumedrol at a dose of 10 mg / kg / day during 3 followed by an oral relay at 1 mg / kg / day with progressive degression, was indicated in 8 cases. Retinal photocoagulation was performed in one patient. The evolution was marked by a regression of inflammatory signs with final visual acuity ≤ 1/10 in 4 patients. Two cases were complicated by extended posterior synechiae with acute ocular hypertonia that required a Yag laser iridotomy after inflammation control. Conclusion: Blindness remains the most serious complication of ocular Behçet disease. The prognosis depends on the precocity of treatment and requires a strong collaboration between ophthalmologists and internists.